Relevant Publications by BARC Investigators

• BARC Publications

• BARC Abstracts

• General

• Clinical Experience

• Basic Research

BARC Publications

DeRusso PA, Ye W, Shepherd RW, Haber BA, Shneider BL, Whitington PF, Schwarz KB, Bezerra JA, Rosenthal P, Karpen S, Squires RH, Magee JC, Robuck PR, Sokol, RJ for the Biliary Atresia Research Consortium. (2007) Growth Failure and Outcomes in Infants with Biliary Atresia: A Report from the Biliary Atresia Research Consortium. Hepatology 2007; 46(5):1632-1638. [P001]

Sokol RJ, Shepherd RW, Superina R, Bezerra JA, Robuck P, Hoofnagle JH. Screening and Outcomes in Biliary Atresia: Summary of a National Institutes of Health Workshop [Reviews]. Hepatology 2007; 46(2):556-581.

Hoofnagle JH. Biliary Atresia Research Consortium (in From the NIH). Hepatology 2004; 39(4):891.

Sokol RJ. New North American Research Network Focuses on Biliary Atresia and Neonatal Liver Disease [News and Views]. Journal of Pediatric Gastroenterology and Nutrition 2003; 36(1):1.

Shneider BL, Brown MB, Haber B, Whitington PF, Schwarz K, Squires R, Bezerra J, Shepherd R, Rosenthal P, Hoofnagle JH, Sokol RJ, BARC. A Multi-Center Study of Biliary Atresia Outcome in the United States (1997-2000). J Pediatr 2006 Apr; 148(4):467-74.

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BARC Abstracts

Haber B, Brown M, Shneider B, Sokol R, Whitington P, DeRusso P, Squires R, Bezerra J, Shepherd R, Rosenthal P, Robuck P and BARC. Patient Demographics and Clinical Practices in a US Multi-center Study of Biliary Atresia. Presented at the American Association for the Study of Liver Diseases, 55th Annual Meeting, Boston, MA, 2004. Hepatology 2004 Oct; 40(S4): 472A.

Shneider B, Brown M, Sokol R, Whitington P, Schwarz K, Squires R, Bucuvalas J, Haber B, Shepherd R, Rosenthal P, Robuck P, and BARC. A Multi-center Analysis of Outcome at 24 Months of Age in Children with Biliary Atresia in the United States. Presented at the American Association for the Study of Liver Diseases, 55th Annual Meeting, Boston, MA, 2004. Hepatology 2004 Oct; 40(S4): 201A.

DeRusso P, Ye W, Haber B, Shneider B, Sokol R, Whitington P, Squires R, Bezerra J, Shepherd R, Rosenthal P, Robuck P. Early Growth Failure following Hepatoportoenterostomy is Associated with Liver Transplantation or Death in Infants with Biliary Atresia. Presented at the American Association for the Study of Liver Diseases, 56th Annual Meeting, San Francisco, CA 2005. Hepatology 2005 Oct; 42(S1): 64A.

Russo P, Boitnott J, Bove K, Brown M, Finegold M, Haas J, Jaffe R, Kim G, Magee J, Magid M, Melin-Aldana H, Sokol R, White F for BARC. A Multi-Institutional Study of Interobserver Agreement on the Histologic Diagnosis of Biliary Obstruction in Liver Biopsies of Cholestatic Infants Less than Six Months of Age. American Association for the Study of Liver Diseases, 57th Annual Meeting, Boston, MA, October 27-31, 2006.

Shneider B, Norton, Superina R, Erlichman J, Magee J, Bucuvalas J, Squires R, Benson J, Karpen S, Shepherd R, Sokol R, BARC (2006) Diagnostic Imaging in Neonatal Cholestasis: A Multi-center Prospective Analysis. American Association for the Study of Liver Diseases, 57th Annual Meeting, Boston, MA, October 27-31, 2006.

Sokol R, Bezerra J, Haber B, Karpen S, Perlmutter D, Rosenthal P, Schwarz K, Shepherd R, Shneider B, Whitington P, Russo P, Superina R, Magee J, Robuck P, Hoofnagle J for BARC (2006) Biliary Atresia Research Consortium (BARC): NIH-funded network to advance knowledge and improve care and outcomes in biliary atresia. Screening and Outcomes in Biliary Atresia, a Research Workshop sponsorted by the National Institute of Diabetes & Digestive & Kidney Diseases, Bethesda, MD, September 11-12, 2006.

Shneider B, Shepherd R, Magee J, Bucuvalas JC, Haber B, Karpen SJ, Rosenthal P, Schwarz KB, Suchy FJ, Whitington PF, Sokol RJ, BARC (2007) Discriminating Features of Biliary Atresia - A Prospective Multi-Centered Analysis. American Association for the Study of Liver Diseases, 58th Annual Meeting, Boston, MA, November 2-6, 2007.

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General Publications

Moyer V, Freese DK, Whitington PF, Olsen AD, Brewer F, Colletti RB, Heyman MB. North American Society for Pediatric Gastroenterology, Hepatology, and Nutrition Guidelines for the Evaluation of Cholestatic Jaundice in Infants: Recommendations of the North American Society for Pediatric Gastroenterology, Hepatology, and Nutrition. J Pediatr Gastroenterol Nutr 2004; Sep 39(3):306.

Hoofnagle JH. Biliary Atresia Reasearch Consortium (BARC). Hepatology 2004; Apr 39(4):891.

Sokol RJ. New North American Research Network Focuses on Biliary Atresia and Neonatal Liver Disease.
J Pediatr Gastroenterol Nutr 2003; Jan 36(1):1.

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Clinical Experience

Utterson EC, Shepherd RW, Sokol RJ, Bucuvalas J, Magee JC, McDiarmid SV, Anand R. The Split Research Group.
Biliary Atresia: Clinical Profiles, Risk Factors, and Outcomes of 755 Patients Listed for Liver Transplantation. J Pediatr 2005; Aug 147(2):180-185.

Tiao GM, Alonso M, Bezerra J, Yazigi N, Heubi J, Balistreri W, Bucuvalas J, Ryckman F. Liver Transplantation in children younger than 1 year – The Cincinnati experience. J Pediatr Surg 2005; Jan 40(1): 268-73; discussion 273.

Condino AA, Ivy DD, O’Connor JA, Narkewicz MR, Mengshol S, Whitworth JR, Clausen L, Doran A, Sokol RJ. Portopulmonary hypertension in pediatric patients. J Pediatr 2005; Jul 147(1):20-6.

Squires RH Jr. From whence does biliary atresia arise? Pediatric Transplant 2005; Apr 9(2):145-7.

Arvay JL, Zemel BS, Gallagher PR, Rovner AJ, Mulberg AE, Stallings VA, Haber BA. Body composition of children aged 1 to 12 years with biliary atresia or Alagille syndrome. J Pediatr Gastroenterol Nutr 2005; Feb 40(2):146-50.

Sokol RJ, Mack CL. Optimizing outcomes and bridging biliary atresia into adulthood. Hepatology 2005; Feb 41(2): 231-3.

Weerasooriya VS, White FV, Shepherd RW. Hepatic fibrosis and survival in biliary atresia. J Pediatr 2004; Jan 144(1):123-5.

Haber BA, Russo P. Biliary atresia. Gastroenterol Clin North Am 2003; Sep 32(3):891-911.

Bucuvalas JC, O’Connor A, Buschle K, Krug S, Ryckman FC, Atherton H, Alonso MP, Balistreri WF. Risk of hearing impairment in pediatric liver transplant recipients: a single center study. Pediatr Transplant 2003; Aug 7(4):265-9.

Sokol RJ, Mack C, Narkewicz MR, Karrer FM. Pathogenesis and outcome of biliary atresia: current concepts. J Pediatr Gastroenterol Nutr 2003; Jul 37(1): 4-21.

DeRusso PA, Spevak MR, Schwarz KB. Fractures in biliary atresia misinterpreted as child abuse. Pediatrics 2003; Jul 112(1 Pt1):185-88.

Tsao K, Rosenthal P, Dhawan K, Danzer E, Sydorak R, Hirose S, Farmer DL, Albanese CT, Harrison MR, Lee H. Comparison of drainage techniques for biliary atresia. J Pediatr Surg 2003; Jul 38(7):1005-7.

Bucuvalas JC, Britto M, Krug S, Ryckman FC, Atherton J, Alonso MP, Balistreri WF, Kotagal. Health-related quality of life in pediatric liver transplant recipients: A single center study. Liver Transpl 2003; Jan 9(1):62-71.

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Basic Research

Carvalho E, Liu C, Shivakumar P, Sabla G, Aronow B, Bezerra JA. Analysis of biliary transcriptome in experimental biliary atresia. Gastroenterology 2005; Aug 129(2):713-7.

Mack CL, Tucker RM, Sokol RJ, Kotzin BL. Armed CD4+Th1 effector cells and activated macrophages participate in bile duct injury in murine biliary atresia. Clin Immunol 2005; May 115(2):200-9.

Mack CL, Sokol RJ. Unraveling the pathogenesis and etiology of biliary atresia. Pediatr Res 2005; May 57(5 Pt2):87R-94R. Epub 2005 Apr 6.

Whitington PF, Malladi P, Melin-Aldana H, Azzam R, Mack CL, Sahai A. Expression of osteopontin correlates with portal biliary proliferation and fibrosis in biliary atresia. Pediatr Res 2005; Jun 57(6):837-44. Epub 2005 Apr 21.

Shivakumar P, Campbell KM, Sabla GE, Miethke A, Tiao G, McNeall MM, Ward RL, Bezerra JA. Obstruction of extrahepatic bile ducts by lymphocytes is regulated by IFN-gamma in experimental biliary atresia. J Clin Invest 2004; Aug 114(3):322-9.

Suskind DL, Rosenthal P, Heyman MB, Kong D, Magrane G, Baxter-Lowe LA, Muench MO. Maternal microchimerism on the livers of patients with biliary atresia. BMC Gastroenterol 2004; Jul 31 4(1):14.

Shivakumar P, Bezerra JA. Biliary atresia and Th1 function: linking lymphocytes and bile ducts: commentary on the article by Mack et al. on page 79. Pediatr Res 2004; Jul 56(1):9-10. Epub 2004 May 5.

Mack CL, Tucker RM, Sokol RJ, Karrer FM, Kotzin BL, Whitington PF, Miller SD. Biliary atresia associated with CD4+Th1 cell-mediated portal tract inflammation. Pediatr Res 2004; Jul 56(1):79-87. Epub 2004 May 5.

Zhang DY, Sabla G, Shivakumar P, Tiao G, Sokol RJ, Mack CL, Shneider BL, Aronow B, Bezerra JA. Coordinate expression of regulatory genes differentiates embryonic and perinatal forms of biliary atresia. Hepatology 2004; Apr 39(4):954-62.

Torbenson M, Wang J, Abraham S, Maitra A, Boitnott J. Bile ducts and ductules are positive for CD56 (N-CAM) in most cases of extrahepatic biliary atresia. Am J Surg Pathol 2003; Nov 27(11):1454-7.

Burch JM, Sokol RJ, Narkewicz MR, Reichlin M, Frank MB, MacKenzie T, Lee LA. Autoantibodies in mothers of children with neonatal liver disease. J Pediatr Gastroenterol Nutr. 2003 Sep;37(3):262-7.

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